Hemangiopericytoma

HEMANGIOPERICYTOMA
FROM THE CAPILLARY PERICYTE(EPITHELIAL ORIGIN) OF ZIMMERMAN
RARE, 20% IN THE H&N
HIGH INCIDENCE ON NASAL SEPTUM—OFTEN PRESENT WITH EPISTAXIS
CAN BE BENIGN OR MALIGNANT
IF MALIGNANT 50% METS TO BONE OR LUNG
MALE = FEMALE, USUALLY IN 4TH, 5TH, AND 6TH DECADES
STAINS + VIMENTIN, FACTOR 8, FACTOR 13
CHARACTERISTIC APPEARANCE WITH SILVER RETICULIN STAIN
PRIMARILY PRESENTS AS A SLOW GROWING PAINLESS MASS
Rx–SURGERY (WLE) IS BEST—TREAT LIKE IT IS MALIGNANT, RELATIVELY RADIORESISTANT

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