CLIVAL CHORDOMA
RARE
FROM VESTIGEAL EMBRYONIC NOTOCHORD(MESENCHYMAL)
SECOND MOST COMMON SIGHT (1/3) FOR A CHORDOMA (FIRST = SACROCOCCYGEAL (2/3))
SLOW GROWING
INVASIVE
PRIMARY SX = HA
PRIMARY PRESENTATION = DIPLOPIA FROM INVASION OF FORAMEN LACERUM–DORELLOS CANAL—LR PAULSEY
USUALLY UNRESECTABLE—HIGH RENT DISTRICT
USALLY LETHAL–HIGH RECURRANCE RATE
BONEY EROSION OF CLIVUS—RETROCELLULAR CALCIFICATIONS
THREE CELL TYPES: PHYSALIPHOROUS(CONTAINS INTRACELULAR MUCIN), STELLATE, AND INTERMEDIATE
TWO TYPES OF CHORDOMA: TYPICAL (WORSE Px) AND CHONDROID (BETTER Px)
Rx–SURGERY, RT CAN BE PALLIATIVE, ?CHEMO