Pilomatricoma

PILOMATRICOMA—”PREVIOUSLY CALLED PILOMATRIXOMA OF MALHERBE”
A CALCIFYING EPITHELIOMA OF MALHERBE (CALCIUM DEPOSITS IN 75%/0SSIFICATION IN 15-20%)
RARE—A BENIGN TUMOR OF HAIR FOLLICLE MATRIX CELL ORIGIN
50% IN THE H&N
PRIMARILY 8-13 YEARS OLD
FEMALE > MALE
ASSOC. WITH MYOTONIC MUSCULAR DYSTROPHY, GARDNER’S SYNDROME, AND CRANIAL DYSOSTOSIS
Rx: WLE—-RECURRENCE IS RARE—-PROBABLY CAN MANAGE EXPECTANTLY AFTER AN EXCISIONAL BIOPSY

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